Open heart operation in a patient with hereditary spherocytosis: a case report.

نویسندگان

  • S Aoyagi
  • H Kawano
  • H Tomoeda
  • R Hiratsuka
  • T Kawara
چکیده

A 9-year-old girl who had ostium secundum atrial septal defect (ASD) and hereditary spherocytosis (HS) is described. The patient had a history of splenectomy for HS and underwent repair of the ASD under cardiopulmonary bypass (CPB), however, no significant or persistent hemolysis was observed during and after CPB. Only 10 patients with HS who underwent cardiac operations using CPB have been reported. The case is presented due to its rarity.

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عنوان ژورنال:
  • Annals of thoracic and cardiovascular surgery : official journal of the Association of Thoracic and Cardiovascular Surgeons of Asia

دوره 7 6  شماره 

صفحات  -

تاریخ انتشار 2001